Amelogênese imperfeita do tipo hipoplásica: relato de dois casos familiares.

Abstract

Amelogenesis imperfecta is a genomic development condition characterized by hypomineralization or hypoplasia with discoloration, sensitivity and fragility through various defects in the enamel matrix, with uncertain etiology and variable patterns of inheritance. It features a variable prevalence depending on the methods of study which is intended to categorization of this condition and the types that features being the hypoplastic variant the most prevalent. This paper reports two cases among patients of the same family who have been diagnosed imperfect amelogenesis of hypoplastic type through clinical and radiographic, relating the condition of heredity characteristics among family members. It is important for the dentist to study and understand these rare entities to discuss clinical management, multidisciplinary and individualized planning, focusing due esthetic and functional aspects, also psychological, should the clinician be aware of the main signs that this condition displays, by its similarity with other defects enamel and require immediate intervention.