Perfil clínico e epidemiológico de pacientes pediátricos com Doença Falciforme internados por crises álgica de um Hospital Universitário de Campina Grande - PB.

Abstract

INTRODUCTION: Sickle cell disease is a genetic condition determined by autosomal recessive inheritance that has great importance in its environment through chronicity and incapacity, associated with several acute complications, among them an allergic crisis. OBJECTIVES: To describe the clinical and epidemiological profile of pediatric patients with sickle cell disease hospitalized with an pain crisis at the University Hospital Alcides Carneiro, since his frist stay in service until december 2017. METHODOLOGY: This is an observational, descriptive cross-sectional study in Data from the medical records were included by analyzing data from pediatric patients with sickle cell disease treated at the University Hospital Alcides Carneiro in Campina Grande, Brazil, who evaluated a sample of 45 patients complications. A statistical analysis was performed by the data rights holder himself. RESULTS: Among the patients analyzed, 51,1% were female, 48,8% were 10 years of age or older, 77,7% were brown and 71,1% lived in cities around Campina Grande. Of the sample, 80,1% had family rents up to a minimum wage; 80,1% belonged to class D-E and 46,7% did not have basic sanitation at home. Among those over seven years of age, 26,7% presented school- age delay; 46,7% of caregivers reported less than nine years of study. Regarding the nutritional status, 82,2% were considered. About the age of diagnosis, 46,6% were diagnosed between two full months of life and five years. A greater percentage, 84,5% of the patients, did not present regular follow-up. Among the acute complications, 97,8% presented an infectious process, 64,5% acute chest syndrome, 4,4% cerebrovascular accident and 4,4% aplastic crisis. Of the number of cases, 31,1% had an average of 5,4 total hospital stay; 28,9% were hospitalized five or more times; Deaths were not verified during the search period. According to the treatment, 66,7% used antimicrobial prophylaxis, with 70% regularity; 40% made/used hydroxyurea. CONCLUSION: The study under discussion reinforced the need for the establishment of policies of care and education for the SCD carriers and their caregivers, as well as for the professionals involved in the appropriate follow-up.